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http://dx.doi.org/10.3340/jkns.2011.49.5.299

Spinal Extradural Meningeal Cyst in Klippel-Trenaunay Syndrome  

Choi, Kyung-Chul (Department of Neurosurgery, Daegu Wooridul Spine Hospital)
Ahn, Sung-Tae (Department of Neurosurgery, Daegu Wooridul Spine Hospital)
Shin, Yong-Hawn (Department of Neurosurgery, Daegu Wooridul Spine Hospital)
Lee, Sang-Ho (Department of Neurosurgery, Wooridul Spine Hospital)
Publication Information
Journal of Korean Neurosurgical Society / v.49, no.5, 2011 , pp. 299-301 More about this Journal
Abstract
A case of a symptomatic spinal extradural meningeal cyst (SEMC) in Klippel-Trenaunay syndrome (KTS) is introduced. A 38-year-old woman presented with right L2 radiculopathy. She underwent operations for varicose veins in both her lower extremities. She had port-wine nevi on her trunk and extremities. The edematous change in both legs had waxed and waned. Magnetic resonance imaging showed an $11.8{\times}13$ mm extradural meningeal cyst growing through the intervertebral foramen in L2-3. Multiple meningeal cysts were located in the dorsal aspect of the spinal cord from T3 to T10. A $5.8{\times}6.2$ mm cyst was also found in left pleural cavity. The extradural meningeal cyst was completely excised and the preoperative symptom was improved. KTS is a congenital disorder due to a mesodermal abnormality, which may predispose the dura to weakness. The SEMC may occur through the dural defect or weakened point.
Keywords
Spinal extradural meningeal cyst; Klippel-Trenaunay syndrome; Mesodermal abnormality;
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