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http://dx.doi.org/10.5762/KAIS.2017.18.12.352

Lower Motor Weakness and Complex Regional Pain Syndrome of Lower Limb in the Patient of Frontotemporal Dementia: A Case Report  

Lee, Kwang Min (Department of Rehabilitation Medicine, Wonkwang University School of Medicine)
Noh, Se Eung (Department of Rehabilitation Medicine, Wonkwang University School of Medicine)
Joo, Min Cheol (Department of Rehabilitation Medicine, Wonkwang University School of Medicine)
Hwang, Yong (Department of Emergency Medicine, Wonkwang University School of Medicine)
Kim, Ji Hee (Department of Rehabilitation Medicine, Wonkwang University School of Medicine)
Publication Information
Journal of the Korea Academia-Industrial cooperation Society / v.18, no.12, 2017 , pp. 352-358 More about this Journal
Abstract
Frontotemporal dementia, the second most common cause of early onset dementia, is a neurodegenerative clinical syndrome characterized by progressive deficits in behavior, executive function and language. Although motor symptoms in frontotemporal dementia are represented by motor neuron disease, parkinsonism and progressive supranuclear palsy syndrome, there have been no reports of motor weakness caused by the direct involvement of central motor nervous systems in frontotemporal dementia. Moreover, no association between clinical dementia groups and complex regional pain syndrome has been reported. We diagnosed a rare case with motor weakness and complex regional pain syndrome of lower limbs due to central nervous system lesion in a patient with frontotemporal dementia by magnetic resonance imaging, electrodiagnostic study and three phase bone scan. Following steroid therapy for complex regional pain syndrome, pain was improved. Functional improvement was noted after rehabilitation therapy, including functional electrical stimulation, muscle strengthening exercise and gait training during hospitalization. This case report suggests that rehabilitation therapy for motor weakness in frontotemporal dementia could be effective for improving overall function.
Keywords
Complex Regional Pain Syndromes; Electromyography; Evoked Potentials; Frontotemporal Dementia; Lower Extremity Paresis; Radionuclide Imaging; Rehabilitation;
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