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http://dx.doi.org/10.4250/jcu.2016.24.2.168

Rare Case of Unileaflet Mitral Valve  

Shah, Jainil (Department of Internal Medicine, Henry Ford Hospital)
Jain, Tarun (Department of Internal Medicine, Henry Ford Hospital)
Shah, Sunay (Department of Cardiology, Henry Ford Hospital)
Mawri, Sagger (Department of Internal Medicine, Henry Ford Hospital)
Ananthasubramaniam, Karthikeyan (Department of Cardiology, Henry Ford Hospital)
Publication Information
Journal of Cardiovascular Imaging / v.24, no.2, 2016 , pp. 168-169 More about this Journal
Abstract
Unileaflet mitral valve is the rarest of the congenital mitral valve anomalies and is usually life threatening in infancy due to severe mitral regurgitation (MR). In most asymptomatic individuals, it is mostly due to hypoplastic posterior mitral leaflet. We present a 22-year-old male with palpitations, who was found to have an echocardiogram revealing an elongated anterior mitral valve leaflet with severely hypoplastic posterior mitral valve leaflet appearing as a unileaflet mitral valve without MR. Our case is one of the 11 reported cases in the literature so far. We hereby review those cases and conclude that these patients are likely to be at risk of developing worsening MR later in their lives.
Keywords
Congenital mitral valve anomaly; Unileaflet mitral valve; Mitral regurgitation;
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