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http://dx.doi.org/10.4250/jcu.2015.23.4.266

A CASE OF KLIPPEL-TRENAUNAY SYNDROME WITH ACUTE SUBMASSIVE PULMONARY THROMBOEMBOLISM TREATED WITH THROMBOLYTIC THERAPY  

Chu, Seong-Taek (Department of Internal Medicine, National Medical Center)
Han, Yung-Hee (Department of Internal Medicine, National Medical Center)
Koh, Jung-A (Department of Internal Medicine, National Medical Center)
Kim, Seon-Jae (Department of Internal Medicine, National Medical Center)
Lee, Hak-Cheol (Department of Internal Medicine, National Medical Center)
Kim, Si-Eun (Department of Internal Medicine, National Medical Center)
Shin, Yong-Chul (Cardiovascular Center, National Medical Center)
Sir, Jung Ju (Department of Internal Medicine, National Medical Center)
Choi, Seung Min (Department of Internal Medicine, National Medical Center)
Joo, Shin Bae (Department of Internal Medicine, National Medical Center)
Publication Information
Journal of Cardiovascular Imaging / v.23, no.4, 2015 , pp. 266-270 More about this Journal
Abstract
Klippel-Trenaunay syndrome is a rare congenital mesodermal abnormality characterized by varicose veins, cutaneous hemangiomas, soft tissue and bony hypertrophy of limb. Potential complications such as deep venous thrombosis and pulmonary thromboembolism have not been reported in Korea to date. We demonstrate the case of a 48-year-old woman with Klippel-Trenaunay syndrome with extensive varicose veins on right lower limb, hypertrophy of left big toe and basilar artery tip aneurysm, complicated with acute submassive pulmonary thromboembolism treated successfully with intravenous thrombolytic therapy.
Keywords
Klippel-Trenaunay syndrome; Venous thromboembolism; Right-sided heart failure; Thrombolytic therapy; Basilar artery aneurysm;
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