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http://dx.doi.org/10.15324/kjcls.2019.51.2.265

Ebstein's Anomaly in Transthoracic Echocardiography: Two Case Reports  

Kim, Sung-Hee (Department of Cardiology, Cheongju St. Mary's Hospital)
Publication Information
Korean Journal of Clinical Laboratory Science / v.51, no.2, 2019 , pp. 265-269 More about this Journal
Abstract
Ebstein's anomaly is attached to the right ventricle with the tricuspid leaf attached to the lower right ventricle without any attachment to the tricuspid annulus. Most patients in their 20s are alive. Patients older than 25 years of age are similar in the incidence of heart failure and sudden death, and survive approximately 70% from 2 years, and 50% from 3 years, from 5% to over 50 years of age. Through this example, Ebstein's anomaly exists in various forms. A 22 year old case with WPW syndrome and those who survived to 77 years of age are reported. The normal heart structure in the apical four-chamber view should be observed on similar lines, even though the tricuspid annulus is slightly lower than the mitral annulus. If not, there will be some doubt regarding this anomaly. Furthermore, echocardiography plays an important role in the diagnosis and prognosis of congenital heart disease.
Keywords
Congenital heart disease; Ebstein's anomaly; WPW syndrome;
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