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http://dx.doi.org/10.14402/jkamprs.2013.35.6.421

Gardner Syndrome Showing Multiple Osteomas in the Jaws  

Kim, Yongsoo (Department of Oral and Maxillofacial Surgery, School of Dentistry, Chonbuk National University)
Lee, Sun Jae (Department of Oral and Maxillofacial Surgery, School of Dentistry, Chonbuk National University)
Baek, Jin-A (Department of Oral and Maxillofacial Surgery, School of Dentistry, Chonbuk National University)
Ko, Seung-O (Department of Oral and Maxillofacial Surgery, School of Dentistry, Chonbuk National University)
Leem, Dae-Ho (Department of Oral and Maxillofacial Surgery, School of Dentistry, Chonbuk National University)
Publication Information
Maxillofacial Plastic and Reconstructive Surgery / v.35, no.6, 2013 , pp. 421-426 More about this Journal
Abstract
Gardner syndrome, an autosomal dominant inherited condition, is a subtype of familial adenomatous polyposis. It causes lesions in bones, skin, and teeth, as well as multiple gastrointestinal polyps, which, if left untreated, become malignant. Because patients with colorectal cancer have a low survival rate, early diagnosis and treatment of Gardner syndrome is critical. Therefore, the characteristic lesions of Gardner disease that appear on the face, jaws, and oral cavity must be understood; these can be evaluated by oral and maxillofacial clinicians. This report describes a case that was diagnosed and treated earlier with the help of a routine oral and maxillofacial examination and has had a seemingly good prognosis so far.
Keywords
Gardner syndrome; Familial adenomatous polyposis; Osteoma;
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Times Cited By KSCI : 2  (Citation Analysis)
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