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Sequential Management of Pierre Robin Sequence: Case Report  

Kim, Bae-Kyung (Department of Oral and Maxillofacial Surgery, College of Dentistry, Kyung Hee University,)
Kwon, Yong-Dae (Department of Oral and Maxillofacial Surgery, College of Dentistry, Kyung Hee University,)
Ryu, Sun-Youl (Department of Oral and Maxillofacial Surgery, College of Dentistry, Chonnam National University)
Choi, Yong-Ha (Department of Oral and Maxillofacial Surgery, College of Dentistry, Kyung Hee University,)
Ohe, Joo-Young (Department of Oral and Maxillofacial Surgery, College of Dentistry, Kyung Hee University,)
Suh, Joon-Ho (Department of Oral and Maxillofacial Surgery, College of Dentistry, Kyung Hee University,)
Ko, Su-Jin (Department of Dentistry, Division of Orthodontics, Eulji General Hospital, Eulji University School of Medicine)
Publication Information
Maxillofacial Plastic and Reconstructive Surgery / v.33, no.3, 2011 , pp. 270-275 More about this Journal
Abstract
Pierre Robin Sequence (PRS) is known as an anomaly consisting of respiratory obstruction with glossoptosis, micrognathia and cleft palate in a newborn. The etiology of PRS is not known, but several factors may be involved simultaneously. Mortality rate of PRS is about 5~30% and the treatment method is divided into both conventional treatments and surgical interventions. If the respiratory obstruction is not resolved by the conventional method, surgical treatment, such as subperiosteal release of the floor of the mouth, tongue-lip adhesion, tracheostomy, distraction osteogenesis may be needed. This study reports a case of PRS in a newborn male at 20 days, with dyspnea and feeding difficulties. Clinical examination showed micrognathia with glossoptosis and cleft palate as the typical PRS triad. We tried surgical intervention with subperiosteal release of the floor of the mouth and tongue-lip adhesion and surgery was successful. At $19^{th}$ months, we also repaired the incomplete cleft palate successfully using 2-Flap palatoplasty.
Keywords
Pierre Robin Sequence; Tongue-Lip Adhesion; Subperiosteal Release of the Floor of Mouth;
Citations & Related Records
Times Cited By KSCI : 2  (Citation Analysis)
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