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LONG TERM FOLLOW-UP OF MULTIPLE ODONTOGENIC KERATOCYSTS ASSOCIATED WITH BASAL CELL NEVUS SYNDROME: A CASE REPORT  

Lee, Eun-Young (Department of Oral & Maxillofacial Surgery, College of Medicine and Medical Research Institute, Chungbuk National University)
Kim, Kyoung-Won (Department of Oral & Maxillofacial Surgery, College of Medicine and Medical Research Institute, Chungbuk National University)
Publication Information
Maxillofacial Plastic and Reconstructive Surgery / v.32, no.1, 2010 , pp. 81-85 More about this Journal
Abstract
Multiple jaw cysts are one of the most constant features of the basal cell nevus syndrome. Basal cell nevus syndrome is inherited as an autosomal dominant trait with variable expressiveness. This syndrome comprises a number of abnormalities such as multiple nevoid basal cell carcinomas of the skin, skeletal abnormalities as bifid rib and fusion of vertebrae, central nervous system abnormalities as mental retardation, eye abnormalities with multiple jaw cysts. The odontogenic keratocysts in patients with this syndrome are often associated with the crowns of unerupted teeth and huge size; on radiographs they may mimic dentigerous cysts. The most important feature of the cyst is its extraordinary recurrence rate. Since recurrence may be long delayed in this lesion, follow-up of any case of odontogenic keratocyst with roentgenograms and clinical examination of basal cell carcinoma are essential for at least five years after surgery. We report the result of 7-year follow up after cyst enucleation associated with basal cell nevus syndrome with the literature of review.
Keywords
Basal cell nevus syndrome; Multiple odontogenic keratocyst;
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Times Cited By KSCI : 1  (Citation Analysis)
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