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http://dx.doi.org/10.12701/yujm.2020.00066

Anti-nuclear antibody-negative immunoglobulin G4-associated autoimmune hepatitis mimicking lymphoproliferative disorders  

Kang, Min Kyu (Department of Internal Medicine, Yeungnam University College of Medicine)
Park, Jung Gil (Department of Internal Medicine, Yeungnam University College of Medicine)
Choi, Joon Hyuk (Department of Pathology, Yeungnam University College of Medicine)
Publication Information
Journal of Yeungnam Medical Science / v.37, no.2, 2020 , pp. 136-140 More about this Journal
Abstract
Immunoglobulin G4 (IgG4)-associated autoimmune hepatitis (AIH) is a very rare subtype of autoimmune hepatitis and characterized by marked elevated serum IgG and hepatic infiltration of IgG4-expressing plasma cells. Pathologic confirmation of hepatic IgG4-expressing plasma cells is usually required for the final diagnosis of IgG4-associated AIH. Herein, we report the case of a 47-year-old female diagnosed with autoantibody-negative IgG4-associated AIH mimicking lymphoproliferative disorders.
Keywords
Autoimmune hepatitis; Immunoglobulin G; Immunoglobulin G4-related disease; Plasma cells; Prednisolone;
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