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http://dx.doi.org/10.12655/KADH.2019.15.1.29

DENTAL MANAGEMENT OF A 46-MONTH-OLD CHILD WITH PRADER-WILLI SYNDROME : A CASE REPORT  

Choi, Kyung Hwa (Department of Pediatric Dentistry, Kyung Hee University Dental Hospital at Gangdong, Kyung Hee University)
Kim, Mi Sun (Department of Pediatric Dentistry, Kyung Hee University Dental Hospital at Gangdong, Kyung Hee University)
Nam, Ok Hyung (Department of Pediatric Dentistry, School of Dentistry, Kyung Hee University)
Lee, Hyo-Seol (Department of Pediatric Dentistry, School of Dentistry, Kyung Hee University)
Choi, Sung Chul (Department of Pediatric Dentistry, School of Dentistry, Kyung Hee University)
Kim, Kwangchul (Department of Pediatric Dentistry, Kyung Hee University Dental Hospital at Gangdong, Kyung Hee University)
Publication Information
The Journal of Korea Assosiation for Disability and Oral Health / v.15, no.1, 2019 , pp. 29-34 More about this Journal
Abstract
Prader-Willi Syndrome (PWS) is a rare neurologic disorder with a prevalence 1/10,000-30,000. The cause of PWS is an abnormalities of chromosome 15q11.2-q13 which is an imprinting gene. Obesity and hyperphagia are characteristic features on a PWS adult. On the other hand, the birth weight, height and body mass index (BMI) of PWS infants are 15-20% lower than those of normal babies and there is a failure to thrive until 24-month-old. Most of PWS patients are treated under general anesthesia and conscious sedation. This case is a treatment of severe caries in a PWS 46 month-old child without general anesthesia and conscious sedation. He came to the Department of Pediatric Dentistry, Kyung Hee University Dental Hospital at Gangdong, Seoul, Korea with a trauma history. He had a medical history with heart surgery and needed to take antibiotics prophylaxis. The luxated left upper primary tooth were removed and caries treatment were done as an outpatient without general anesthesia, conscious sedation.
Keywords
Prader-Willi Syndrome; Outpatient treatment of PWS; Trauma of PWS;
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