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http://dx.doi.org/10.12655/KADH.2018.14.1.41

DENTAL CHARACTERISTICS OF A PATIENT WITH MCCUNE-ALBRIGHT SYNDROME  

Lim, Jae-Young (Department of Pediatric Dentistry, College of Dentistry, Yonsei University)
Song, Je-Seon (Department of Pediatric Dentistry, College of Dentistry, Yonsei University)
Lee, KoEun (Department of Pediatric Dentistry, College of Dentistry, Yonsei University)
Lee, Jae-Ho (Department of Pediatric Dentistry, College of Dentistry, Yonsei University)
Publication Information
The Journal of Korea Assosiation for Disability and Oral Health / v.14, no.1, 2018 , pp. 41-44 More about this Journal
Abstract
McCune-Albright syndrome (MAS) is a rare disease characterized by fibrous dysplasia (FD), Cafe-au-lait spots, and endocrine disorder. A 4-year-old girl with MAS visited the clinic with a chief complaint of facial asymmetry and bruxism without any pain. Facial asymmetry and many dental problems such as midline deviation, "ground glass appearance" on the entire jaw, thinned cortical bone, loss of lamina dura and ectopic germs were found. Because of severely displaced tooth germs and FD affected jaw, there is a high possibility of malocclusion during mixed/permanent dentition. It is necessary to observe the eruption pattern periodically. If there are clinical symptoms like an abnormal eruption pattern, facial asymmetry or high caries susceptibility, appropriate interventions of dentist are required.
Keywords
McCune-Albright syndrome; Fibrous dysplasia; Facial asymmetry;
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