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http://dx.doi.org/10.12655/jkdoh.2013.9.1.42

CARIES TREATMENT OF A 4-YEAR-OLD FEMALE PATIENT WITH DE GROUCHY SYNDROME UNDER GENERAL ANESTHESIA : A CASE REPORT  

Song, Jisoo (Department of Pediatric Dentistry, School of Dentistry, Seoul National University)
Lee, Euj-Ji (Department of Pediatric Dentistry, School of Dentistry, Seoul National University)
Shin, Teo-Jeon (Department of Pediatric Dentistry, School of Dentistry, Seoul National University)
Hyun, Hong-Keun (Department of Pediatric Dentistry, School of Dentistry, Seoul National University)
Kim, Jung-Wook (Department of Pediatric Dentistry, School of Dentistry, Seoul National University)
Jang, Ki-Taeg (Department of Pediatric Dentistry, School of Dentistry, Seoul National University)
Lee, Sang-Hoon (Department of Pediatric Dentistry, School of Dentistry, Seoul National University)
Kim, Chong-Chul (Department of Pediatric Dentistry, School of Dentistry, Seoul National University)
Kim, Young-Jae (Department of Pediatric Dentistry, School of Dentistry, Seoul National University)
Publication Information
The Journal of Korea Assosiation for Disability and Oral Health / v.9, no.1, 2013 , pp. 42-45 More about this Journal
Abstract
De Grouchy syndrome or Distal 18q- is a genetic condition caused by a deletion of genetic material within chromosome 18, and the deletion involves the distal section of 18q. It causes a wide range of medical and developmental concerns. Congenital orthopedic anomalies, cleft lip and palate are relatively common. People with distal 18q- are often small for their age. Most individuals with distal 18q- fall in the mild to moderate range of intellectual disability. Strabismus and nystagmus, changes in the optic nerve as well as colobomas are also fairly common. People with distal 18q- frequently have conductive and/or sensorineural hearing loss. At present, treatment for distal 18q- is only symptomatic. This article presents a case report: Caries treatment of a 4-year-old female patient with de Grouchy syndrome under general anesthesia. The special considerations of dental care, especially caries treatment for the patient with de Grouchy syndrome are discussed.
Keywords
de Grouchy syndrome; Distal 18q-; Dental caries; General anesthesia;
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