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A Case of Hereditary Hemorrhagic Telangiectasia Managed withIntranasal Topical Estrogen  

Song, Jeong-Hwan (아주대학교)
Kim, Hyeon-Jun (아주대학교)
Yun, Yong-Ro (아주대학교)
Kim, Yun-Tae (아주대학교)
Publication Information
Korean Journal of Otorhinolaryngology-Head and Neck Surgery / v.49, no.4, 2006 , pp. 447-450 More about this Journal
Abstract
Hereditary hemorrhagic telangiectasia is an autosomal dominant disorder affecting blood vessels of the skin, mucous membrane and viscera. It is characterized by a clinical triad of multiple telangiectasia, recurrent hemorrhages and familial occurrence. In 80% of patients, epistaxia is the first presenting symptom. It can have a massive impact on the quality of life of those affected. Otolaryngologists should be familiar with this disease because of its potential systemic complication. Recently, we have experienced a 69 year old female complaining of melena and recurrent epistaxis for 20 years. Epistaxis was successfully managed with topical estrogen ointment.
Keywords
Hereditary hemorrhagic telangiectasia; Epistaxis; Estrogen;
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Times Cited By KSCI : 1  (Citation Analysis)
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