[KSCI] Korea Science Citation Index Service

http://dx.doi.org/10.5090/jcs.20.132

Multiple Primary Cardiac Malignant Peripheral Nerve Sheath Tumors in the Left Atrium: Case Report

Li, Junfei (Department of Cardiac Surgery, Affiliated Hospital of Guizhou Medical University)
Chen, Qiansu (Department of Cardiac Surgery, Affiliated Hospital of Guizhou Medical University)
Yu, Shaomei (Department of Ultrasound, Affiliated Hospital of Guizhou Medical University)
Yang, Siyuan (Department of Cardiac Surgery, Affiliated Hospital of Guizhou Medical University)

Publication Information

Journal of Chest Surgery / v.54, no.5, 2021 , pp. 422-424 More about this Journal

Abstract

Malignant peripheral nerve sheath tumors are rare sarcomas of the heart. Herein, we report the case of a 24-year-old man who complained of dyspnea, cough, and upper left back pain. He was found to have multiple primary heart tumors obstructing the right superior pulmonary vein in the left atrium, which were diagnosed as malignant peripheral nerve sheath tumors. The patient underwent successful resection of the tumors and immunohistochemistry was utilized for diagnosis.

Keywords

Neurogenic tumor; Neurofibrosarcoma; Heart neoplasms; Case report;

Citations & Related Records

Reference

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