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http://dx.doi.org/10.5090/kjtcs.2018.51.1.64

Hughes-Stovin Syndrome as an Outcome of Behçet Disease or as a Different Entity  

Demirkan, Serkan (Department of Dermatology and Venerology, Kirikkale University Faculty of Medicine)
Gultekin, Yildirim (Department of Cardiovascular Surgery, Kirikkale University Faculty of Medicine)
Publication Information
Journal of Chest Surgery / v.51, no.1, 2018 , pp. 64-68 More about this Journal
Abstract
Hughes-Stovin syndrome is a rare disorder of unknown etiology. Although the association between multiple pulmonary artery aneurysms and venous thrombosis of the lower limbs was reported by Beattie and Hall in 1911, it was not until 1962 that the eponym "Hughes-Stovin syndrome" was formally introduced in the medical literature. We describe 2 patients with Hughes-Stovin syndrome who presented with pulmonary artery aneurysm, thrombophlebitis, hemoptysis, and oral ulcers, review the manifestations of the disease, and compare its similarities with and differences from Behçet disease.
Keywords
Hughes-Stovin syndrome; Behcet disease; Pulmonary artery aneurysms; Thrombosis; Oral ulcer;
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Times Cited By KSCI : 1  (Citation Analysis)
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