[KSCI] Korea Science Citation Index Service

http://dx.doi.org/10.5090/kjtcs.2014.47.6.536

Multiple Aortic Operations in Loeys-Dietz Syndrome: Report of 2 Cases

Na, Kwon Joong (Department of Thoracic and Cardiovascular Surgery, Seoul National University Bundang Hospital, Seoul National University College of Medicine)
Park, Kay-Hyun (Department of Thoracic and Cardiovascular Surgery, Seoul National University Bundang Hospital, Seoul National University College of Medicine)

Publication Information

Journal of Chest Surgery / v.47, no.6, 2014 , pp. 536-540 More about this Journal

Abstract

Due to its low prevalence and because there is lack of awareness about it, Loeys-Dietz syndrome is often misdiagnosed as Marfan syndrome, which has similar skeletal abnormalities and aortic pathology. However, the differential diagnosis between these two connective tissue diseases is critical because they correspond to different surgical indications and surgical decision-making. We report two cases of successful thoracoabdominal aortic replacement in patients with previously undiagnosed Loeys-Dietz syndrome.

Keywords

Loeys-Dietz syndrome; Marfan syndrome; Aortic aneurysm; Aorta, surgery;

Citations & Related Records

Times Cited By KSCI : 1 (Citation Analysis)

Reference
Cited By KSCI

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