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http://dx.doi.org/10.5090/kjtcs.2010.43.5.518

Right Ventricle Exclusion in Severe Neonatal Ebstein's Anomaly  

Min, Sun-Kyung (Department of Thoracic and Cardiovascular Surgery, Seoul Paik Hospital, Inje University School of Medicine)
Kim, Woong-Han (Department of Thoracic and Cardiovascular Surgery, College of Medicine, Seoul National University)
Lee, Young-Ok (Department of Thoracic and Cardiovascular Surgery, College of Medicine, Seoul National University)
Seong, Yong-Won (Department of Thoracic and Cardiovascular Surgery, College of Medicine, Seoul National University)
Park, Sung-Joon (Department of Thoracic and Cardiovascular Surgery, College of Medicine, Seoul National University)
Choi, Jin-Ho (Department of Thoracic and Cardiovascular Surgery, College of Medicine, Seoul National University)
Publication Information
Journal of Chest Surgery / v.43, no.5, 2010 , pp. 518-521 More about this Journal
Abstract
A one-day-old baby was transferred for cyanosis and heart murmur. Echocardiographic evaluation revealed that he had severe neonatal Ebstein's anomaly (Carpentier type C), pulmonary atresia, and pulmonary circulation via patent ductus arteriosus. Because the wall of the atrialized right ventricle was very thin, showed decreased contractility, and the small right ventricle showed pulmonary atresia, we decided that a two-ventricular repair was impossible. When the patient was one-month-old, he underwent right atrium reduction-plasty, a right ventricular exclusion procedure (including atrialized right ventricle resection and functional right ventricle plication), and right modified Blalock-Taussig shunt. He was discharged without specific problems. He received a bidirectional cavopulmonary shunt successfully at 4 months later.
Keywords
Right ventricle; Congenital heart disease; Ebstein's anomaly;
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Times Cited By KSCI : 2  (Citation Analysis)
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