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Aggressive Surgical Treatment for Complex Cardiac Anomalies Associated with Right Atrial Isomerism  

Hwang, Ui-Dong (Division of Pediatric Cardiac Surgery, Asan Medical Center, University of Ulsan College of Medicine)
Jung, Sung-Ho (Division of Pediatric Cardiac Surgery, Asan Medical Center, University of Ulsan College of Medicine)
Jhang, Won-Kyoung (Division of Pediatric Cardiac Surgery, Asan Medical Center, University of Ulsan College of Medicine)
Kim, Young-Hwue (Division of Pediatric Cardiology, Asan Medical Center, University of Ulsan College of Medicine)
Yun, Tae-Jin (Division of Pediatric Cardiac Surgery, Asan Medical Center, University of Ulsan College of Medicine)
Publication Information
Journal of Chest Surgery / v.40, no.8, 2007 , pp. 569-573 More about this Journal
Abstract
A 3 month old female baby, who had been diagnosed with right atrial isomerism associated with total anomalous pulmonary venous return (TAPVR), a functional single ventricle and major aortopulmonary collateral arteries (MAPCA), underwent left MAPCA unifocalization and left Blalock-Taussig shunt (3.5 mm) at 3 months of age. The post-operative course was complicated by pulmonary venous congestion, and the drainage site of the TAPVR was found to be stenotic on echocardiography. We performed sutureless repair of the TAPVR along with unifocalization of the right MAPCA. She was put on an extracorporeal membrane oxygenator for 8 days after the 2nd operation, and she was able to come off the oxygenator with the placement of a central shunt (3 mm). She developed tracheal stenosis, which was presumably due to longstanding endotracheal intubation, and she then underwent tracheostomy. She was discharged to home on day 104 after the 1st operation, and she has been followed up for 2 months in a good clinical condition.
Keywords
Heterotaxy; Pulmonary vein total anomalous return; Pulmonary artery, collateral; Extracorporeal membrane oxygenation;
Citations & Related Records
Times Cited By KSCI : 1  (Citation Analysis)
연도 인용수 순위
1 Freedom RM, Jaeggi ET, Lim JS, Anderson RH. Heart with isomerism of right atrial appendages - one of the worst forms of disease in 2005. Cardiol Young 2005;15:554-67   DOI   ScienceOn
2 Park JS, Chang YH, Jun TG, et al. Congenital pulmonary vein stenosis with normal anatomical connection. Korean J Thorac Cardiovasc Surg 2004;37:364-8
3 Yun TJ, Al-Radi OO, Adatia I, et al. Contemporary management of right atrial isomerism: effect of evolving therapeutic strategies. J Thorac Cardiovasc Surg 2006;131:1108-13   DOI   ScienceOn
4 Kumar S, Ansari J, Weerasena N. A rare association of major aorto-pulmonary collaterals with right isomerism and totally anomalous pulmonary venous drainage. Cardiol Young 2005;15:643-6   DOI   ScienceOn