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A Communicating Bronchopulmonary Foregut Malformation Associated with Absence of the Left Pericardium - A case report -  

Yoo, Dong-Gon (Department of Thoracic & Cardiovascular Surgery, Gangneung Asan Hospital, University of Ulsan College of Medicine)
Park, Chong-Bin (Department of Thoracic & Cardiovascular Surgery, Gangneung Asan Hospital, University of Ulsan College of Medicine)
Kang, Pil-Je (Department of Thoracic and Cardiovascular Surgery, Asan Medical Center, University of Ulsan College of Medicine)
Lee, Jong-Hyeog (Department of Diagnostic Radiology, Gangneung Asan Hospital, University of Ulsan College of Medicine)
Kim, Chong-Wook (Department of Thoracic & Cardiovascular Surgery, Gangneung Asan Hospital, University of Ulsan College of Medicine)
Publication Information
Journal of Chest Surgery / v.40, no.11, 2007 , pp. 793-797 More about this Journal
Abstract
A communicating bronchopulmonary foregut malformation (CBPFM) is a rare congenital anomaly that is characterized by a fistula between isolated respiratory tissue and the esophagus or stomach, The presence of accessory lung tissue arising from the primitive gastrointestinal tube is a common factor in the development of all forms of bronchopulmonary foregut malformations. Recurrent pneumonia associated with cystic radiographic structures is a characteristic of the condition. Further imaging studies using esophagogram, bronchography, computerized tomography, MRI, and arteriography can help in making a diagnostic evaluation. The treatment is a surgical resection of the involved lung tissue, and fistula closure with a good prognosis. We encountered a case of CBPFM, who presented with an extralobar pulmonary sequestration and bronchogenic cyst communicating with a tubular esophageal duplication that was associated with a complete left pericardial defect.
Keywords
Esophageal congenital anomalies; Lung anomaly; Pericardium;
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