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Modified Starnes Operation for Neonatal Stenotic Ebstein Anomaly  

Lee Seung Hyun (Division of Pediatric Cardiac Surgery, Asan Medical Center, University of Ulsan College of Medicine)
Yun Tae-Jin (Division of Pediatric Cardiac Surgery, Asan Medical Center, University of Ulsan College of Medicine)
Publication Information
Journal of Chest Surgery / v.38, no.9, 2005 , pp. 633-636 More about this Journal
Abstract
Sixteen-day-old baby with severe Ebstein anomaly underwent emergency operation to relieve progressive hypoxia and congestive heart failure. Operative findings showed huge right atrium and atrialized right ventricle (aRV) with very small functional RV by distal displacemcent of tricuspid valve mechanism. We elected to perform modified Starness operation because biventricular repair was deemed unattainable. After pulmonary and tricuspid valves were primarily closed, aRV was obliterated with multiple sutures from RV apex to the base. Then a PTFE (Gore-Tex, USA) vascular graft was interposed between innominate artery and main pulmonary artery for systemic to pulmonary shunt. The patient was discharged uneventfully, and received bi-directional cavopulmonary shunt 6 months later.
Keywords
Congenital heart disease; Ebstein's anomaly; Surgery method;
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