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Congenital Pulmonary Vein Stenosis with Normal Anatomical Connection -One case report-  

박준석 (성균관대학교 의과대학 삼성서울병원 흉부외과)
장윤희 (부천세종병원 흉부외과)
정미진 (단국대학교병원 소아과)
강이석 (성균관대학교 의과대학 삼성서울병원 소아과)
전태국 (성균관대학교 의과대학 삼성서울병원 흉부외과)
Publication Information
Journal of Chest Surgery / v.37, no.4, 2004 , pp. 364-368 More about this Journal
Abstract
Congenital pulmonary vein stenosis is a rare anomaly and related to high mortality due to progressive pulmonary hypertension and heart failure in infancy. Aggressive anti-failure medication and surgical treatment is recommended. Surgical options are balloon dilatation, endovascular stent, pneumonectomy, lung transplantation, patch grafting, and sutureless repair. We report a case of congenital pulmonary vein stenosis with normal anatomical connection successfully treated with sutureless technique and using pulmonary vasodilators, such as Sildenafil, lloprost and iNO postoperatively.
Keywords
Pulmonary veins; Suture; Surgery method; Congenital heart defect;
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