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Single Lung Transplantation in the Patient with End-stage Lymphangioleiomyomatosis -Report of 1 case-  

양희철 (성균관대학교 의과대학 삼성서울병원 흉부외과)
최용수 (성균관대학교 의과대학 삼성서울병원 흉부외과)
김진국 (성균관대학교 의과대학 삼성서울병원 흉부외과)
심영목 (성균관대학교 의과대학 삼성서울병원 흉부외과)
김관민 (성균관대학교 의과대학 삼성서울병원 흉부외과)
Publication Information
Journal of Chest Surgery / v.37, no.12, 2004 , pp. 1015-1018 More about this Journal
Abstract
Lymphangioleiomyomatosis (LAM) is a rare disease in women in childbearing age leading to progressive respiratory failure. LAM is characterized by an abnormal harmartomatous proliferation of smooth muscle cells surrounding the blood vessels, lymphatics and airways in the lung. This proliferation leads to airway obstruction, cystic alveolar change and lymphatic obstruction. Patients present with dyspnea, pneumothorax, cough, chest pain, hemoptysis, and chylous effusion. Although lung transplantation is the only therapeutic modality in end-stage LAM with respiratory failure, there has not been any report of successful treatment in Korea. We report one case of successful left single lung transplantation in a 40 year old woman suffering from end-stage LAM.
Keywords
Lung transplantation; Lymphangioleiomyomatosis;
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