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Interrupted Aortic Arch with Apical Muscular Ventricular Septal Defect Associating Esophageal Atresia with Tracheoesophageal Fistula  

조정수 (부산대학교 의과대학 흉부외과학교실)
이형두 (부산대학교 의과대학 소아과학교실)
Publication Information
Journal of Chest Surgery / v.37, no.10, 2004 , pp. 856-860 More about this Journal
Abstract
Interrupted aortic arch with concomitant intracardiac defects is a rare congenital anomaly that has an unfavorable natural course. We report a successful staged operation of interrupted aortic arch with apical muscular ventricular septal defect associating esophageal atresia with tracheoesophageal fistula in a 3-day-old neonate weighing 2.6 kg. We repaired esophageal atresia through the right thoracotomy and subsequently performed extended end-to-end anastomosis of the aortic arch with pulmonary artery banding through the left thoracotomy at same operation. The apical muscular VSD was repaired 87 day after first operation. The patient required multiple additional interventions before closure of the apical muscular ventricular septal defect, such as pyloromyotomy for idiopathic hypertrophic pyloric stenosis, anterior aortopexy for airway obstruction, and balloon aortoplasty for residual coarctation. She is now doing well.
Keywords
Aortic arch; interrupted; Heart septal defect; ventricular; Esophageal stresia; Tracheoesophageal fistula; Aortic arch;
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