Browse > Article

Aortic Root Replacement in Patient of Right Ventricular Hypoplasia with Annuloaortic Ectasia, Ventricular Septal Defect and Aortic Regurgitation - Report of 1 case -  

Baek, Man-Jong (Dept. of Thoracic and Cardiovascular Surgery, Sejong General Hospital, Sejong Heart Institute)
Na, Chan-Young (Dept. of Thoracic and Cardiovascular Surgery, Sejong General Hospital, Sejong Heart Institute)
Oh, Sam-Se (Dept. of Thoracic and Cardiovascular Surgery, Sejong General Hospital, Sejong Heart Institute)
Kim, Woong-Han (Dept. of Thoracic and Cardiovascular Surgery, Sejong General Hospital, Sejong Heart Institute)
Whang, Sung-Wook (Dept. of Thoracic and Cardiovascular Surgery, Sejong General Hospital, Sejong Heart Institute)
Lee, Cheol (Dept. of Thoracic and Cardiovascular Surgery, Sejong General Hospital, Sejong Heart Institute)
Chang, Yun-Hee (Dept. of Thoracic and Cardiovascular Surgery, Sejong General Hospital, Sejong Heart Institute)
Jo, Won-Min (Dept. of Thoracic and Cardiovascular Surgery, Sejong General Hospital, Sejong Heart Institute)
Kim, Jae-Hyun (Dept. of Thoracic and Cardiovascular Surgery, Sejong General Hospital, Sejong Heart Institute)
Seo, Hong-Ju (Dept. of Thoracic and Cardiovascular Surgery, Sejong General Hospital, Sejong Heart Institute)
Kang, Sang-Soo (Dept. of Anesthesiology, and Pain Clinic, College of Medicine, Hallym University)
Moon, Hyun-Soo (Dept. of Anesthesiology, and Pain Clinic, College of Medicine, Hallym University)
Park, Young-Kwan (Dept. of Thoracic and Cardiovascular Surgery, Sejong General Hospital, Sejong Heart Institute)
Kim, Chong-Whan (Dept. of Thoracic and Cardiovascular Surgery, Sejong General Hospital, Sejong Heart Institute)
Publication Information
Journal of Chest Surgery / v.36, no.7, 2003 , pp. 510-513 More about this Journal
Abstract
Annuloaortic ectasia, aortic regurgitation(AR), and ventricular septal defect(VSD) in patients with right ventricular hypoplasia is a very rare condition. We report a patient who underwent aortic root replacement with a composite graft for annuloaortic ectasia associated with VSD and AR in right ventricular hypoplasia. The patient was a 19 year-old male. Transthoraic echocardiogram and cardiac catheterization revealed a perimembranous VSD (2 cm in diameter), severe AR, annuloaortic ectasia, bipartite right ventricle with hapoplasia, and hypoplastic tricuspid valve. Operative findings showed that free margins of the right and noncoronary cusps were markedly elongated, thickened, and retracted, and commissure between the right coronary cusp and the noncoronary cusp was fused and calcified. VSD was closed with an autologous pericardial patch and composite graft aortic root replacement using direct coronary button reimplantation was performed, and the hypertrophic muscle of the right ventricular outflow tract was resected. The patient had transient weaning failure of cardiopulmonary bypass and was discharged at the postoperative 14 days without any problems.
Keywords
Hypoplastic right ventricle; Heart septal defect, ventricular; Aortic valve insufficiency; Annuloaortic ectasia; Bentall operationx;
Citations & Related Records
Times Cited By KSCI : 1  (Citation Analysis)
연도 인용수 순위
1 Valve-preserving aortic replacement: Does the additinoal repair of leaflet prolapse adversely affect the results? /
[ Langer,F.;Graeter,T.;Nikoloudakis,N.;Aicher,D.;Wendler,O.;Schafers,H.J. ] / J Thorac Cardiovasc Surg   DOI   ScienceOn
2 Aortic valve sparing operations: an update /
[ David,T.E.;Armstrong,S.;Ivanov,J.;Webb,G.D. ] / Ann Thorac Surg   DOI   ScienceOn
3 Remodeling of the aortic annulus /
[ Sarsam,M.A.;Yacoub,M.H. ] / J Thorac Cardiovasc Surg
4 Anatomic correction of the syndrome of prolapsing right coronary aortic cusp, dilatation of the sinus of Valsalva, and ventricular septal defect /
[ Yacoub,M.H.;Khan,H.;Stavri,G.;Shinebourne,E.;Radley-Smith,R. ] / J Thorac Cardiovasc Surg   DOI   ScienceOn
5 Late results of a valve-preserving operation in patients with aneurysm of the ascending aorta and root /
[ Yacoub,M.H.;Gehle,P.;Chandrasekaran,V.;Birks,E.J.;Child,A.;Radley-Smith,R. ] / J Thorac Cardiovasc Surg   DOI   ScienceOn
6 An aortic valve-sparing operation for patients with aortic incompetence and aneurysm of the ascending aorta /
[ David,T.E.;Feindel,C.M. ] / AnJ Thorac Cardiovase Surg
7 Composite valve graft를 이용한 대동맥근부 치환술 /
[ 백만종;나찬영;김웅한(등) ] / 대흉외지   과학기술학회마을
8 Single coronary artery assocoated with annuloaortic ectasia and ventricular septal defect /
[ Kallikazaros,J.E.;Gavaliatsis,I.P.;Tentolouris,C.A.(et al.) ] / Cathet Cardiovasc Diagn   DOI   ScienceOn