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Biventricular Repair of Critically III Neonate with Ebstein′s Anomaly - Report of 1 case -  

Kong, Joon-Hyuk (Department of Thoracic and Cardiovascular Surgery, Sejong General Hospital, Sejong Heart Institute)
Kim, Woong-Han (Department of Thoracic and Cardiovascular Surgery, Sejong General Hospital, Sejong Heart Institute)
Ryu, Jae-Wook (Department of Thoracic and Cardiovascular Surgery, Sejong General Hospital, Sejong Heart Institute)
Lee, Seog-Ki (Department of Thoracic and Cardiovascular Surgery, College of Medicine, Chosun University)
Baek, Man-Jong (Department of Thoracic and Cardiovascular Surgery, Sejong General Hospital, Sejong Heart Institute)
Lim, Cheong (Department of Thoracic and Cardiovascular Surgery, Sejong General Hospital, Sejong Heart Institute)
Kim, Soo-Cheol (Department of Thoracic and Cardiovascular Surgery, Sejong General Hospital, Sejong Heart Institute)
Oh, Sam-Se (Department of Thoracic and Cardiovascular Surgery, Sejong General Hospital, Sejong Heart Institute)
Na, Chan-Young (Department of Thoracic and Cardiovascular Surgery, Sejong General Hospital, Sejong Heart Institute)
Kim, Soo-Jin (Department of Pediatric Cardiology, Sejong General Hospital, Sejong Heart Institute)
Park, Young-Kwan (Department of Thoracic and Cardiovascular Surgery, Sejong General Hospital, Sejong Heart Institute)
Kim, Chong-Whan (Department of Thoracic and Cardiovascular Surgery, Sejong General Hospital, Sejong Heart Institute)
Publication Information
Journal of Chest Surgery / v.35, no.4, 2002 , pp. 303-306 More about this Journal
Abstract
Patients with severe Ebstein's anomaly showing in the neonatal period, represent progressive cardiac enlargement with pulmonary hypoplasia and functional pulmonary atresia with patent ductus alteriosus-dependent pulmonary circulation. Biventricular repair in these patients had been mostly unsuccessful except for Starnes' procedure that converts the anatomy to single ventricle physiology for Fontan procedure. A 4-days old male was admitted with the diagnosis of severe Ebstein's anomaly with anatomic pulmonary atresia and severe cardiac enlargement. He successfully underwent biventricular repair with vertical plication method of atrialized right ventricle, tricupid annuloplasty, transannular right ventricular outflow tract reconstrulltion, atrial septal defect patch closure with fenestration, and right atrial reduction angioplasty Postoperatively, cardiothoracic ratio was significantly reduced and mild tricuspid regurgitation was remnant in echocardiography. The patient is currently 10 months old and is fully active without restrictions.
Keywords
Ebstein′s anomaly; Neonate; Surgery method;
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  • Reference
1 Natural history of Ebstein's anomaly of tricuspid valve in childhood and adolescence: an international cooperative study of 505 cases. /
[ Watson H. ] / Br Heart J
2 Ebstein's anomaly: echocardiographic and clinical features in the fetus and neonates. /
[ Roberson DA;Silverman NH. ] / J Am Coll Cardiol   DOI
3 Outcome in cyanotic neonates with Ebstein's anomaly. /
[ Yetman AT;Freedom RM;McCrindle BW. ] / Am J Cardiol   DOI
4 Tricuspid valve diasease with significant tricuspid insufficiency in the fetus: diagnosis and outcome. /
[ Hornberger LK;Sahn DJ;Kleinman CS(et al) ] / J Am Coll Cardiol   DOI
5 Ebstein's anomaly appearing in the neonate, A new surgical approach. /
[ Starnes VA;Pitlick PT;Bernstein D(et al) ] / J Thorac Cardiovasc Surg
6 Neonatal repair of Ebstein's anomaly: indications, surgical technique, and medium-term follow up. /
[ Knott-Craig CJ;Overholt ED;Ward KE;Razook JD. ] / Ann Thorac Surg   DOI   ScienceOn
7 Three cases of neonatal Ebstein's anomaly with remarkable cardiomegaly. /
[ Tanaka T;Kan T;Yamada M(et al) ] / Jpn J Pediatr Cardiol
8 Outcome in neonates with Ebstein's anomaly. /
[ Celermajer DS;Cullen S;Sullivan ID(et al) ] / J Am Coll Cardiol   DOI