[KSCI] Korea Science Citation Index Service

Cor Triatriatum with Infracardiac Total Anomalous Pulmonary Venous Drainage

Man Jong Baek (Department of Thoracic and Cardiovascular Surgery Sejong General Hospital, Sejong Heart Institute)
Woong-Han Kim (Department of Thoracic and Cardiovascular Surgery Sejong General Hospital, Sejong Heart Institute)
Chan Young Na (Department of Thoracic and Cardiovascular Surgery Sejong General Hospital, Sejong Heart Institute)
Sam Se Oh (Department of Thoracic and Cardiovascular Surgery Sejong General Hospital, Sejong Heart Institute)
Soo Cheol Kim (Department of Thoracic and Cardiovascular Surgery Sejong General Hospital, Sejong Heart Institute)
Jae young Lee (Pediatric Cardiology, Sejong General Hospital, Sejong Heart Institute)
Yang Bin Jeon (Department of Thoracic and Cardiovascular Surgery, Gachon Medical College, Gil Heart Center)
Seog Ki Lee (Department of Thoracic and Cardiovascular Surgery, Chosun University Hospital)
Chang-Ha Lee (Department of Thoracic and Cardiovascular Surgery, Gachon Medical College, Gil Heart Center)

Publication Information

Journal of Chest Surgery / v.35, no.1, 2002 , pp. 52-55 More about this Journal

Abstract

We report one case of an 18-day-old female patient, weighing 3.4 kg, with severe cyanosis. The diagnosis was made with only transthoracic echocardiography, which revealed cor triatriatum with an atretic small opening of fibromuscular membrane, obstructive infracardiac total anomalous pulmonary venous drainage(TAPVD), severely restrictive interatrial communication, and scanty mitral inflow and aortic forward flow. The preoperative decision-making for biventricular repair was not easy due to collapsed left heart system caused by remarkably reduced blood flow An emergent operation was performed due to severe cyanosis. All left heart structures were somewhat hypoplastic but thought to be adequate for systemic circulation. Biventricular repair was done without specific intraoperative problems. The postoperative course was uneventful. The patient has been doing well with no evidence of pulmonary vein stenosis or mitral regurgitation for 4 months after operation.

Keywords

Cor triatriatum; Pulmonary vein, total anomalous return;

Citations & Related Records

Reference

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