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http://dx.doi.org/10.5624/isd.2019.49.4.307

Case series of cleidocranial dysplasia: Radiographic follow-up study of delayed eruption of impacted permanent teeth  

Yeom, Han-Gyeol (Department of Oral and Maxillofacial Radiology, Research Institute of Dental Education, College of Dentistry, Wonkwang University)
Park, Won-Jong (Department of Oral and Maxillofacial Surgery, Research Institute of Dental Education, College of Dentistry, Wonkwang University)
Choi, Eun Joo (Department of Oral and Maxillofacial Surgery, Research Institute of Dental Education, College of Dentistry, Wonkwang University)
Kang, Kyung-Hwa (Department of Orthodontics, Research Institute of Dental Education, College of Dentistry, Wonkwang University)
Lee, Byung-Do (Department of Oral and Maxillofacial Radiology, Research Institute of Dental Education, College of Dentistry, Wonkwang University)
Publication Information
Imaging Science in Dentistry / v.49, no.4, 2019 , pp. 307-315 More about this Journal
Abstract
This report describes 3 cases of cleidocranial dysplasia (CCD) and presents relevant findings on long-term follow-up radiographic images of impacted permanent teeth with delayed eruption. Radiographic images of 3 CCD patients were reviewed retrospectively. These images were mainly composed of panoramic and skull radiographs, and the follow-up periods were 3, 13, and 13 years, respectively. The distinct features revealed by the images were described, and the eruption state of impacted permanent teeth was evaluated. The features common to the 3 cases were multiple supernumerary teeth, the presence of Wormian bone, underdevelopment of the maxilla and the maxillary sinus, and clavicular hypoplasia. The eruption of impacted permanent teeth was not observed without proper dental treatment in adult CCD cases, even after long time periods had elapsed. When proper orthodontic force was applied, tooth movement was observed in a manner not significantly different from the general population.
Keywords
Cleidocranial Dysplasia; Jaw; Radiography;
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