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A Case of Lymphangioleiomyomatosis Combined with Chylothorax and Bilateral Pneumothoraces  

Kim, Jong-Hwa (Division of Respiratory & Allergy Medicine, Department of Internal Medicine, Soonchunhyang University, School of Medicine)
Kim, Yang-Ki (Division of Respiratory & Allergy Medicine, Department of Internal Medicine, Soonchunhyang University, School of Medicine)
Kim, Jung-Hyun (Division of Respiratory & Allergy Medicine, Department of Internal Medicine, Soonchunhyang University, School of Medicine)
Lee, Young Mok (Division of Respiratory & Allergy Medicine, Department of Internal Medicine, Soonchunhyang University, School of Medicine)
Kim, Ki-Up (Division of Respiratory & Allergy Medicine, Department of Internal Medicine, Soonchunhyang University, School of Medicine)
Uh, Soo-taek (Division of Respiratory & Allergy Medicine, Department of Internal Medicine, Soonchunhyang University, School of Medicine)
Noh, Hyung-Jun (Department of Radiology, Soonchunhyang University, School of Medicine)
Kim, Hyun Jo (Department of Chest Surgery, Soonchunhyang University, School of Medicine)
Jang, Won Ho (Department of Chest Surgery, Soonchunhyang University, School of Medicine)
Kim, Dong-Won (Department of Clinical Pathology, Soonchunhyang University, School of Medicine)
Publication Information
Tuberculosis and Respiratory Diseases / v.62, no.6, 2007 , pp. 554-559 More about this Journal
Abstract
A 29-year-old female patient presented with exertional dyspnea that she had suffered with for 2 months. The chest X-ray displayed right pleural effusion that was diagnosed as chyle, according to the level of cholesterol and triglyceride in the pleural fluid. VATS (video assisted thoracic surgery) of the right lung was performed on the 7th day of hospitalization for obtaining a lung biopsy and to control the of pneumochylothorax. On the 11th hospitalization day, VATS of left lung was also performed to control the recurrent pneumothorax via pleurodesis. The lung biopsy showed moderate amounts of spindle-shaped and rounded cells (so-called LAM cells), which were reactive to actin and HMB45 (on immunohistochemical stains). We report here on a rare case of lymphangioleiomyomatosis combined with chylothorax and bilateral pneumothroraces.
Keywords
Lymphangioleiomyomatosis; Chylothorax; Pneumothorax;
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