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http://dx.doi.org/10.5125/jkaoms.2022.48.6.386

Management of multiple odontogenic keratocysts associated with nevoid basal cell carcinoma syndrome: a case report of 11-year follow-up  

Hoon-Min, Kim (Department of Oral and Maxillofacial Surgery, Ulsan University Hospital, University of Ulsan College of Medicine)
Se-Jeong, Lim (Department of Oral and Maxillofacial Surgery, Ulsan University Hospital, University of Ulsan College of Medicine)
Yeong-Cheol, Cho (Department of Oral and Maxillofacial Surgery, Ulsan University Hospital, University of Ulsan College of Medicine)
Iel-Yong, Sung (Department of Oral and Maxillofacial Surgery, Ulsan University Hospital, University of Ulsan College of Medicine)
Jang-Ho, Son (Department of Oral and Maxillofacial Surgery, Ulsan University Hospital, University of Ulsan College of Medicine)
Publication Information
Journal of the Korean Association of Oral and Maxillofacial Surgeons / v.48, no.6, 2022 , pp. 386-389 More about this Journal
Abstract
Multiple odontogenic keratocysts (OKC) are a distinguishing feature of nevoid basal cell carcinoma syndrome (NBCCS). Owing to the high recurrence rate of syndromes associated OKCs, complete surgical resection is generally recommended as a definitive treatment. Herein, we report the management of multiple OKCs with marsupialization followed by excision with peripheral ostectomy in an NBCCS patient. We then discuss lesion progression over 11 years of annual follow-ups.
Keywords
Odontogenic cysts; Decompression; Recurrence;
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1 Evans DG, Ladusans EJ, Rimmer S, Burnell LD, Thakker N, Farndon PA. Complications of the naevoid basal cell carcinoma syndrome: results of a population based study. J Med Genet 1993;30:460-4. https://doi.org/10.1136/jmg.30.6.460   DOI
2 Kimonis VE, Goldstein AM, Pastakia B, Yang ML, Kase R, DiGiovanna JJ, et al. Clinical manifestations in 105 persons with nevoid basal cell carcinoma syndrome. Am J Med Genet 1997;69:299-308.
3 Myoung H, Hong SP, Hong SD, Lee JI, Lim CY, Choung PH, et al. Odontogenic keratocyst: review of 256 cases for recurrence and clinicopathologic parameters. Oral Surg Oral Med Oral Pathol Oral Radiol Endod 2001;91:328-33. https://doi.org/10.1067/moe.2001.113109   DOI
4 Manfredi M, Vescovi P, Bonanini M, Porter S. Nevoid basal cell carcinoma syndrome: a review of the literature. Int J Oral Maxillofac Surg 2004;33:117-24. https://doi.org/10.1054/ijom.2003.0435   DOI
5 Chapelle KA, Stoelinga PJ, de Wilde PC, Brouns JJ, Voorsmit RA. Rational approach to diagnosis and treatment of ameloblastomas and odontogenic keratocysts. Br J Oral Maxillofac Surg 2004;42:381-90. https://doi.org/10.1016/j.bjoms.2004.04.005   DOI
6 Stoelinga PJ. Long-term follow-up on keratocysts treated according to a defined protocol. Int J Oral Maxillofac Surg 2001;30:14-25. https://doi.org/10.1054/ijom.2000.0027   DOI
7 Chrcanovic BR, Gomez RS. Recurrence probability for keratocystic odontogenic tumors: an analysis of 6427 cases. J Craniomaxillofac Surg 2017;45:244-51. https://doi.org/10.1016/j.jcms.2016.11.010   DOI
8 Jarisch. Zur lehre von den hautgeschwulsten. Arch Dermat Syph 1894;28:163-222. German. https://doi.org/10.1007/BF01843725   DOI
9 Bakaeen G, Rajab LD, Sawair FA, Hamdan MA, Dallal ND. Nevoid basal cell carcinoma syndrome: a review of the literature and a report of a case. Int J Paediatr Dent 2004;14:279-87. https://doi.org/10.1111/j.1365-263X.2004.00560.x   DOI
10 Gorlin RJ. Nevoid basal cell carcinoma (Gorlin) syndrome: unanswered issues. J Lab Clin Med 1999;134:551-2. https://doi. org/10.1016/s0022-2143(99)90092-6   DOI
11 Kakarantza-Angelopoulou E, Nicolatou O. Odontogenic keratocysts: clinicopathologic study of 87 cases. J Oral Maxillofac Surg 1990;48:593-9; discussion 599-600. https://doi.org/10.1016/s0278-2391(10)80472-0   DOI
12 Littler BO. Gorlin's syndrome and the heart. Br J Oral Surg 1979;17:135-46. https://doi.org/10.1016/s0007-117x(79)80041-4   DOI
13 Vedtofte P, Praetorius F. Recurrence of the odontogenic keratocyst in relation to clinical and histological features. A 20-year followup study of 72 patients. Int J Oral Surg 1979;8:412-20. https://doi. org/10.1016/s0300-9785(79)80079-4   DOI
14 Noy D, Rachmiel A, Zar K, Emodi O, Nagler RM. Sporadic versus syndromic keratocysts-can we predict treatment outcome? A review of 102 cysts. Oral Dis 2017;23:1058-65. https://doi.org/10.1111/odi.12687   DOI