Browse > Article
http://dx.doi.org/10.3348/kjr.2014.15.1.54

Monosegmental Hepatobiliary Fibropolycystic Disease Mimicking a Mass: Report of Three Cases  

Kwon, Jung Hyeok (Department of Radiology, Keimyung University School of Medicine, Dongsan Medical Center)
Kim, Mi Jeong (Department of Radiology, Keimyung University School of Medicine, Dongsan Medical Center)
Kim, Young Hwan (Department of Radiology, Keimyung University School of Medicine, Dongsan Medical Center)
Kang, Koo Jeong (Department of Hepatobiliary Surgery, Keimyung University School of Medicine, Dongsan Medical Center)
Kang, Yu Na (Department of Pathology, Keimyung University School of Medicine, Dongsan Medical Center)
Kwon, Sun Young (Department of Pathology, Keimyung University School of Medicine, Dongsan Medical Center)
Publication Information
Korean Journal of Radiology / v.15, no.1, 2014 , pp. 54-60 More about this Journal
Abstract
Hepatobiliary fibropolycystic diseases are a unique group of entities involving the liver and biliary tract, which are caused by abnormal embryologic development of the ductal plates at various stages. We experienced strange hepatobiliary fibropolycystic diseases with a complex mass composed of malformed ducts and biliary cysts, which did not belong to, and were different from, previously known malformations. They were unique in imaging and histologic features. We herein report three cases of monosegmental hepatobiliary fibropolycystic disease mimicking a mass.
Keywords
Ductal plate malformations; Fibropolycystic disease; Monosegmental disease; Caroli disease;
Citations & Related Records
Times Cited By KSCI : 1  (Citation Analysis)
연도 인용수 순위
1 Brancatelli G, Federle MP, Vilgrain V, Vullierme MP, Marin D, Lagalla R. Fibropolycystic liver disease: CT and MR imaging findings. Radiographics 2005;25:659-670   DOI   ScienceOn
2 Levy AD, Rohrmann CA Jr, Murakata LA, Lonergan GJ. Caroli's disease: radiologic spectrum with pathologic correlation. AJR Am J Roentgenol 2002;179:1053-1057   DOI   ScienceOn
3 Terada T, Moriki T. Monolobar hepatobiliary fibropolycystic disease. Pathol Oncol Res 2011;17:159-165   DOI
4 Terada T, Moriki T. Monolobar ductal plate malformation disease of the liver. Pathol Int 2010;60:407-412   DOI
5 Desmet VJ. Congenital diseases of intrahepatic bile ducts: variations on the theme "ductal plate malformation". Hepatology 1992;16:1069-1083   DOI
6 Summerfield JA, Nagafuchi Y, Sherlock S, Cadafalch J, Scheuer PJ. Hepatobiliary fibropolycystic diseases. A clinical and histological review of 51 patients. J Hepatol 1986;2:141-156   DOI   ScienceOn
7 Veigel MC, Prescott-Focht J, Rodriguez MG, Zinati R, Shao L, Moore CA, et al. Fibropolycystic liver disease in children. Pediatr Radiol 2009;39:317-327; quiz 420-421   DOI
8 Lee HK, Park SJ, Yi BH, Lee AL, Moon JH, Chang YW. Imaging features of adult choledochal cysts: a pictorial review. Korean J Radiol 2009;10:71-80   DOI   ScienceOn
9 Venkatanarasimha N, Thomas R, Armstrong EM, Shirley JF, Fox BM, Jackson SA. Imaging features of ductal plate malformations in adults. Clin Radiol 2011;66:1086-1093   DOI
10 Choi BI, Yeon KM, Kim SH, Han MC. Caroli disease: central dot sign in CT. Radiology 1990;174:161-163   DOI