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http://dx.doi.org/10.3348/kjr.2013.14.4.692

Uncommon of the Uncommon: Malignant Perivascular Epithelioid Cell Tumor of the Lung  

Lim, Hyun-ju (Department of Radiology and Center for Imaging, Samsung Medical Center, Sungkyunkwan University School of Medicine)
Lee, Ho Yun (Department of Radiology and Center for Imaging, Samsung Medical Center, Sungkyunkwan University School of Medicine)
Han, Joungho (Department of Pathology, Samsung Medical Center, Sungkyunkwan University School of Medicine)
Choi, Yong Soo (Department of Thoracic Surgery, Samsung Medical Center, Sungkyunkwan University School of Medicine)
Lee, Kyung Soo (Department of Radiology and Center for Imaging, Samsung Medical Center, Sungkyunkwan University School of Medicine)
Publication Information
Korean Journal of Radiology / v.14, no.4, 2013 , pp. 692-696 More about this Journal
Abstract
A perivascular epithelioid cell (PEC) tumor is a rare mesenchymal tumor characterized by abundant cytoplasmic Periodic acid-Schiff positive glycogen (also called sugar tumor or clear cell tumor of the lung for this characteristic) and is mostly benign. We report a case of a 63-year-old man who presented with an enlarging mass on chest radiograph. After a thorough workup, diagnosis of malignant pulmonary PEC tumor with lung to lung metastases was established. Herein, the difficulties of diagnosis and management we confronted are described.
Keywords
Perivascular epithelioid cell; Pecoma; Clear cell sugar tumor; Lung tumor;
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