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A Case Report of Palatoplasty in a Patient with Clotting Factor Ⅹ Deficiency  

Kim, Suk Wha (Department of Plastic and Reconstructive Surgery, Seoul National University College of Medicine)
Jeong, Eui Cheol (Department of Plastic and Reconstructive Surgery, Seoul National University College of Medicine)
Yun, Byung Min (Department of Plastic and Reconstructive Surgery, Korea University College of Medicine)
Choi, Tae Hyun (Department of Plastic and Reconstructive Surgery, Seoul National University College of Medicine)
Kang, Hyoung Jin (Department of Pediatrics, Seoul National University College of Medicine)
Publication Information
Archives of Plastic Surgery / v.36, no.6, 2009 , pp. 792-794 More about this Journal
Abstract
Purpose: Clotting factor X deficiency is one of the most uncommon coagulation disorders. The authors describe a case of cleft palate in a patient with a congenital clotting factor X deficiency. Methods: In pediatric patients with a cleft palate, the coagulation problem is more worrisome, because they are more sensitive to blood than adults, and because postoperative bleeding can cause blood ingestion with subsequent vomiting, aspiration, and airway obstruction. To prevent hemorrhagic complications in the described case, fresh frozen plasma (FFP) was administered every 24 hrs from the day before surgery to the second postoperative day. Results: Good hemostasis, normal healing, and no complications was shown postoperatively. Conclusion: The replacement of fresh frozen plasma was useful in the case of congenital clotting factor deficiency for bleeding prophylaxis in cleft palate operation.
Keywords
Cleft palate; Clotting factor X deficiency; Bleeding prophylaxis;
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