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Correction of Frontal bone defect in Cleidocranial Dysostosis with Porous Polyethylene(Medpor®): A case report  

Moh, Jae Seong (Department of Plastic & Reconstructive Surgery, Wonkwang University Hospital)
Na, Young Cheon (Department of Plastic & Reconstructive Surgery, Wonkwang University Hospital)
Publication Information
Archives of Plastic Surgery / v.36, no.4, 2009 , pp. 481-484 More about this Journal
Abstract
Purpose: Cleidocranial dysostosis is a rare hereditary disorder affecting bones that develop by intramembranous formation. The typical features include excessive growth of transverse diameter of the skull, hypoplastic clavicles, low height and characteristic facial features. Methods: A 28 years old female patient visited by frontal area depression. The diagnosis was performed by computed tomographic study and radiographic imaging. The patient has widely opened anterior fontanelle, partial fused metopic suture, multiple wormian bone and supernumenary impacted teeth. Under the coronal incision, we exposed depressed frontal area and corrected with Medpor block carving. Results: Postoperatively, frontoparietal skull was aestheticlly improved and she was satisfied with the results. Conclusion: Authors report a case of cleiodocranial dysostosis who has been done correction of abnormal skull shape by Medpor$^{(R)}$ insertion.
Keywords
Cleidocranial dysostosis; Medpor$^{(R)}$;
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