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http://dx.doi.org/10.14253/kjcn.2015.17.1.28

A Fatal Case of Full-Blown Neuro-Behcet Disease  

Na, Boo Suk (Department of Neurology, College of Medicine, Kyung Hee University)
Kwon, Young Nam (Department of Neurology, College of Medicine, Kyung Hee University)
Song, Soo Jin (Department of Neurology, College of Medicine, Kyung Hee University)
Song, Jong Min (Department of Neurology, College of Medicine, Kyung Hee University)
Woo, Ho Geol (Department of Neurology, College of Medicine, Kyung Hee University)
Lee, Dokyung (Department of Neurology, College of Medicine, Kyung Hee University)
Ahn, Tae-Beom (Department of Neurology, College of Medicine, Kyung Hee University)
Publication Information
Annals of Clinical Neurophysiology / v.17, no.1, 2015 , pp. 28-30 More about this Journal
Abstract
We reported a 48-year-old man with Behcet disease, who presented with right hemiparesis. His first brain MRI showed multiple enhanced lesions. During the recovery, he had an episode of left 6th nerve palsy without new lesions in a follow-up MRI. Third episode was cervical myelitis, resulting in respiratory difficulty and quadriplegia without any reflexes. The myelitis was not responsive to immunotherapy. He died of respiratory failure complicated with pneumonia. This is a rare case of full-blown neuro-Behcet disease.
Keywords
Behcet disease; Neuro-Behcet disease; Brainstem; Spinal cord;
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