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A Case of Patulous Eustachian Tube Associated with Kennedy Disease  

Kim, Nam-Hee (Department of Neurology, Dongguk University Ilsan Hospital)
Cho, Chang-Gun (Department of Otorhinolaryngology-Head and Neck Surgery, Dongguk University Ilsan Hospital)
Publication Information
Annals of Clinical Neurophysiology / v.12, no.2, 2010 , pp. 70-72 More about this Journal
Abstract
We report a 53-year-old male having Kennedy disease who complained of severe bilateral tinnitus and autophony. He was diagnosed as patulous Eustachian tube based on the observation of fluttering motion of the tympanic membrane associated with respiration, which is presumed to occur secondary to bulbar weakness. The patulous Eustachian tube affected the management of his respiratory problem by impairing his ability to tolerate BiPAP. We report this rare condition with a literature review.
Keywords
Kennedy disease; Spinobulbar muscular atrophy; Eustachian tube;
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