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http://dx.doi.org/10.3345/kjp.2008.51.9.1018

A case of testicular adrenal rest tumor in a male child with congenital adrenal hyperplasia  

Kim, Joo Hwa (Department of Pediatrics, College of Medicine, Seoul National University)
Yun, Kyong Ah (Department of Pediatrics, College of Medicine, Seoul National University)
Shin, Choong Ho (Department of Pediatrics, College of Medicine, Seoul National University)
Yang, Sei Won (Department of Pediatrics, College of Medicine, Seoul National University)
Publication Information
Clinical and Experimental Pediatrics / v.51, no.9, 2008 , pp. 1018-1022 More about this Journal
Abstract
Testicular adrenal rest tumors are a well-known complication in male patients with congenital adrenal hyperplasia. Corticosteroid suppressive therapy usually results in the regression of these tumors. We describe a patient with 21-hydroxylase deficiency who developed bilateral testicular masses. Despite steroid suppressive therapy, the tumors did not regress and hormonal control was poor. Consequently, bilateral partial orchiectomies were performed.
Keywords
Testicular neoplasms; Adrenal rest tumor; Child; Congenital adrenal hyperplasia; Steroid; 21-hydroxylase;
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Times Cited By KSCI : 1  (Citation Analysis)
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