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A case of adrenocortical adenoma following long-term treatment in a patient with congenital adrenal hyperplasia  

Lho, Seung Rim (Department of Pediatrics, College of Medicine, The Catholic University of Korea)
Park, So Hyun (Department of Pediatrics, College of Medicine, The Catholic University of Korea)
Jung, Min Ho (Department of Pediatrics, College of Medicine, The Catholic University of Korea)
Lee, Byung Churl (Department of Pediatrics, College of Medicine, The Catholic University of Korea)
Publication Information
Clinical and Experimental Pediatrics / v.50, no.3, 2007 , pp. 302-305 More about this Journal
Abstract
As a result of the widespread use and enhanced quality of high-resolution radiological techniques, a recent report has revealed a relatively high prevalence of small adrenal tumors in patients with untreated congenital adrenal hyperplasia due to 21-hydroxylase deficiency. However, there are scarcely any pediatric cases of adrenocortical tumor following long-term treatment in patients suffering with congenital adrenal hyperplasia. We report here on a pediatric female case of adrenocortical adenoma despite adequate long-term treatment for the salt-losing type of congenital adrenal hyperplasia.
Keywords
Congenital adrenal hyperplasia; Adrenocortical tumor;
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