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A case of PFAPA (periodic fever, aphthous stomatitis, pharyngitis, cervical adenitis) syndrome  

Chae, Joo Hee (Department of Pediatrics, College of Medicine, The Catholic University of Korea)
Hwang, A Rum (Department of Pediatrics, College of Medicine, The Catholic University of Korea)
Park, So Hyun (Department of Pediatrics, College of Medicine, The Catholic University of Korea)
Suh, Byung Kyu (Department of Pediatrics, College of Medicine, The Catholic University of Korea)
Publication Information
Clinical and Experimental Pediatrics / v.49, no.9, 2006 , pp. 991-995 More about this Journal
Abstract
PFAPA (periodic fever, aphthous stomatitis, pharyngitis, cervical adenitis) syndrome is one of the causes of periodic fever in pediatrics with unknown etiology. It is characterized by abrupt onset of fever, malaise, aphthous stomatitis, pharyngitis and cervical adenitis without long-term sequelae. Laboratory findings of this sporadic and nonhereditary syndrome are so non-specific that the diagnosis is based on clinical findings. Oral prednisolone is quite effective in controlling the symptoms. We report a case of a 6-year-old girl who was diagnosed as having PFAPA syndrome after 2 years of episodes, by excluding other disease entities with similar clinical features. The patient was treated with oral prednisolone and her symptoms improved dramatically.
Keywords
Periodic fever; Aphthous stomatitis; Pharyngitis; Cervical adenitis; Prednisolone;
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