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A Case of Atypical Teratoid/Rhabdoid Tumor Arising from the Supratentorial Area  

Jung, Kyeong Hun (Department of Pediatrics, College of Medicine, Inha University)
Kwon, Young Se (Department of Pediatrics, College of Medicine, Inha University)
Jun, Yong Hun (Department of Pediatrics, College of Medicine, Inha University)
Kim, Soon Ki (Department of Pediatrics, College of Medicine, Inha University)
Hong, Young Jin (Department of Pediatrics, College of Medicine, Inha University)
Son, Byong Kwan (Department of Pediatrics, College of Medicine, Inha University)
Kim, Eun Young (Department of Neurosurgery, College of Medicine, Inha University)
Park, In Suh (Department of Pathology,College of Medicine, Inha University)
Publication Information
Clinical and Experimental Pediatrics / v.48, no.2, 2005 , pp. 228-231 More about this Journal
Abstract
Atypical teratoid/rhabdoid tumor may arise at any central nervous system location, but it is most commonly located in the cerebellum(60 percent). The incidence of this tumor remains unclear but it occurs most commonly in children less than 2 years of age. This highly malignant tumor shows a rapid progression and nonspecific radiologic findings. We report a case of primary intracranial atypical teratoid/rhabdoid tumor arising from the supratentorial area in early infancy. The diagnosis was made based on distinctive light microscopy and immunohistochemical findings. Despite aggressive surgical treatment with adjuvant chemotherapy, he died six months after his second operation.
Keywords
Atypical teratoid/rhabdoid tumor; Supratentorium;
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1 Burger PC, Yu IT, Tihan T, Friedman HS, Strother DR, Kepner JL, et al. Atypical teratoid/rhabdoid tumor of the central nervous system : a highly malignant tumor of infancy and childhood frequently mistaken for medulloblastoma : a Pediatric Oncology Group study. Am J Surg Pathol 1998; 22:1083-92   DOI   ScienceOn
2 Bhattacharjee M, Hicks J, Langford L, Dauser R, Strother D, Chintagumpala M, et al. Central nervous system atypical teratoid/rhabdoid tumors of infancy and childhood. Ultrastruct Pathol 1997;21:369-78   DOI   ScienceOn
3 Biegel JA, Allen CS, Kawasaki K, Shimizu N, Budarf ML, Bell CJ. Narrowing the critical region for a rhabdoid tumor locus in 22q11. Genes Chromosomes Cancer 1996;16:94-105   DOI   ScienceOn
4 Packer RJ, Biegel JA, Blaney S, Finlay J, Geyer JR, Heideman R, et al. Atypical teratoid/rhabdoid tumor of the central nervous system : report on workshop. J Pediatr Hematol Oncol 2002;24:337-342   DOI   ScienceOn
5 Bonin JN, Rubinstein LJ, Palmer NF, Beckwith JB. The association of embryonal tumors originating in the kidney and in the brain. A report of seven cases. Cancer 1984;54:2137-46   DOI   PUBMED   ScienceOn
6 Beigel JA, Rorke LB, Packer RJ, Emanuel BS. Monosomy 22 in rhabdoid or atypical tumors of the brain. J Neurosurg 1990;73:710-4   DOI   PUBMED
7 Rorke LB, Packer R, Biegel J. Central nervous system atypical teratoid/rhabdoid tumors of infancy and childhood. J Neurooncol 1995;24:21-8   DOI   ScienceOn
8 Lefkowitz IB, Rorke LB, Packer RJ, Sutton LN, Siegel KR, Katnick RJ. Atypical teratoid tumor of infancy : definition of an entity. Ann Neurol 1987;22:448-9
9 Rorke LB, Packer R, Biegel J. Central nervous system atypical teratoid/rhabdoid tumors of infancy and childhood : definition of an entity. J Neurosurg 1996;85:56-65   DOI   ScienceOn
10 Ho DM, Hsu CY, Wong TT, Ting LT, Chiang H. Atypical teratoid/rhabdoid tumor of the central nervous system : a comparative study with primitive neuroectodermal tumor/medulloblastoma. Acta Neuropathol 2000;99:482-8   DOI   ScienceOn
11 Beckwith JB, Palmer NF. Histopathology and prognosis of Wilm's tumor. Results from the First National Wilm's Tumor Study. Cancer 1978;41:1937-48   DOI   PUBMED   ScienceOn