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http://dx.doi.org/10.3904/kjm.2014.87.6.710

A Case of IgG4-Related Pancreas and Kidney Disease Mimicking a Renal Pelvic Malignancy  

Kim, Woo Jae (Department of Internal Medicine, Dong-A University College of Medicine)
Noh, Myung Hwan (Department of Internal Medicine, Dong-A University College of Medicine)
Ryu, Choong Heon (Department of Internal Medicine, Dong-A University College of Medicine)
Han, Seung Hee (Department of Internal Medicine, Dong-A University College of Medicine)
Nam, Hwa Seong (Department of Internal Medicine, Dong-A University College of Medicine)
Han, Ji Eun (Department of Internal Medicine, Dong-A University College of Medicine)
Hong, Sook Hee (Department of Pathology, Dong-A University College of Medicine)
Publication Information
The Korean Journal of Medicine / v.87, no.6, 2014 , pp. 710-715 More about this Journal
Abstract
IgG4-related sclerosing disease is a disease entity that has recently attracted attention, manifesting as a multiorgan disease characterized by high serum IgG4 levels, extensive IgG4-positive plasma cells and lymphocyte infiltration of the affected organs, with the pancreas (autoimmune pancreatitis) and kidney as representative targets. In cases of renal involvement, parenchymal lesions are predominant, such as renal cortical lesions or diffuse renal enlargement. However, mass-like lesions involving the renal pelvis are very rare, and mass forming or pelvic involvement types should be distinguished from lymphomas, metastatic cancers and other genitourinary malignancies to avoid unnecessary surgery. Herein, we report a case of IgG4-related sclerosing disease involving the kidney as an unusual involvement pattern presenting as a mass-like lesion with pelvic and perirenal involvement.
Keywords
IgG4-related kidney disease; Autoimmune pancreatitis; Renal pelvic mass;
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