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http://dx.doi.org/10.3904/kjm.2013.85.2.205

Autosomal Dominant Polycystic Kidney Disease with an Asymptomatic Type I Choledochal Cyst  

Ryu, Seung Jee (Department of Internal Medicine, The Catholic University of Korea College of Medicine)
Kim, Kyung Hoon (Department of Internal Medicine, The Catholic University of Korea College of Medicine)
Kim, Tae Wan (Department of Internal Medicine, The Catholic University of Korea College of Medicine)
Ban, Woo Ho (Department of Internal Medicine, The Catholic University of Korea College of Medicine)
Lee, Su Lim (Department of Radiology, The Catholic University of Korea College of Medicine)
Kim, Sung Soo (Department of Internal Medicine, The Catholic University of Korea College of Medicine)
Kim, Young Ok (Department of Internal Medicine, The Catholic University of Korea College of Medicine)
Publication Information
The Korean Journal of Medicine / v.85, no.2, 2013 , pp. 205-209 More about this Journal
Abstract
Autosomal dominant polycystic kidney disease (ADPKD) is the most common inherited renal disease. Polycystic liver disease is commonly observed in ADPKD but rarely has it been associated with a choledochal cyst. We report a case of a choledochal cyst with ADPKD in a 60-year-old female patient with ADPKD and concomitant chronic renal failure who was admitted because of acute deterioration of kidney function due to poor oral intake. There was no history of a biliary disorder and her kidney function recovered promptly after fluid replacement. Non-enhanced computed tomography was performed to evaluate ADPKD and revealed numerous cysts in both kidneys and liver. It also showed fusiform dilatation of the extrahepatic bile ducts, a finding indicative of a choledochal cyst. Liver function was within the normal range and there was no evidence of extrahepatic biliary obstruction. Magnetic resonance cholangiopancreatography confirmed the diagnosis of a type I choledochal cyst combined with ADPKD.
Keywords
ADPKD; Choledochal cyst; Polycystic liver disease;
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