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http://dx.doi.org/10.3904/kjm.2012.83.2.283

A Case of Pneumatosis Cystoides Intestinalis in a Patient with Systemic Lupus Erythematosus  

Park, Jun-Won (Department of Internal Medicine, Seoul National University College of Medicine)
Song, Yeong-Wook (Department of Internal Medicine, Seoul National University College of Medicine)
Shin, Ki-Chul (Department of Internal Medicine, Seoul National University College of Medicine)
Publication Information
The Korean Journal of Medicine / v.83, no.2, 2012 , pp. 283-286 More about this Journal
Abstract
Pneumatosis cystoides intestinalis, which is characterized by multiple air-filled cysts in the intestinal mucosa, submucosa, and subserosa, is associated with autoimmune disorders, including systemic sclerosis, inflammatory myopathy and, rarely, systemic lupus erythematosus (SLE). Here, we report the case of a 57-year-old female with a 2-year history of SLE who developed pneumatosis cystoides intestinalis. The patient's symptoms were improved with conservative management. Although pneumatosis cystoides intestinalis is an uncommon manifestation of SLE, and follows a mainly benign course, it can be associated with vasculitis, which has a poor prognosis.
Keywords
Pneumatosis cystoides intestinalis; Lupus erythematosus; Systemic; Prednisolone;
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