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A Case of POEMS Syndrome Associated with Idiopathic Liver Cirrhosis  

Ko, Kwang-Hun (Department of Internal Medicine, School of Medicine, Chungnam National University)
Jung, Jae-Hoon (Department of Internal Medicine, School of Medicine, Chungnam National University)
Moon, Hee-Seok (Department of Internal Medicine, School of Medicine, Chungnam National University)
Seong, Jae-Kyu (Department of Internal Medicine, School of Medicine, Chungnam National University)
Kim, Seok-Hyun (Department of Internal Medicine, School of Medicine, Chungnam National University)
Lee, Byung-Seok (Department of Internal Medicine, School of Medicine, Chungnam National University)
Lee, Heon-Young (Department of Internal Medicine, School of Medicine, Chungnam National University)
Publication Information
The Korean Journal of Medicine / v.80, no.5, 2011 , pp. 578-582 More about this Journal
Abstract
POEMS syndrome (polyneuropathy, organomegaly, endocrinopathy, monoclonal gammopathy and skin lesion) is rare multisystemdisease of unknown cause with varying clinical manifestations. Although there is no established definition for this syndrome,the common classical features are considered to be secondary to the plasma cell dyscrasia with the production of a monoclonalcomponent. Anasarca, including ascites, peripheral edema, and pleural effusion, occurs frequently in POEMS syndrome, butcases with idiopathic liver cirrhosis are rarely reported. We experienced a 73-year-old female with POEMS syndrome whose mainproblem was massive ascites. It is the first report of idiopathic liver cirrhosis in a patient with POEMS syndrome in Korea.
Keywords
POEMS syndrome; Ascites; Liver cirrhosis;
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