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http://dx.doi.org/10.17245/jdapm.2020.20.1.49

Difficult intubation caused by an immature upper airway in a patient with cri-du-chat syndrome: a case report  

So, Eunsun (Department of Anesthesiology, School of Dentistry, Dankook University)
Kim, Seungoh (Department of Anesthesiology, School of Dentistry, Dankook University)
Publication Information
Journal of Dental Anesthesia and Pain Medicine / v.20, no.1, 2020 , pp. 49-53 More about this Journal
Abstract
Cri-du-chat syndrome (CdCS) is caused by the deletion of the short arm of chromosome 5. Most patients with CdCS develop intellectual disabilities. Therefore, they have poor oral hygiene and a high caries index. However, treating such patients is not an easy task, because of the difficulty in communication. General anesthesia may be a useful option in adult patients with CdCS and intellectual disability. General anesthesia should be administered very carefully, owing to the presence of comorbid diseases, which may need airway management. Infants with CdCS need general anesthesia if they have a concomitant cardiac anomaly. Intubation is reportedly difficult for such patients was, owing to the structural and functional abnormalities in the larynx and vocal cords. The purpose of this study was to report a case of difficult intubation while inducing general anesthesia in a patient with CdCS during dental treatment, due to a narrow larynx and trachea.
Keywords
Airway Management; Anesthesia; Congenital Abnormalities; Cri-du-Chat Syndrome; Outpatients;
Citations & Related Records
Times Cited By KSCI : 4  (Citation Analysis)
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