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Dental Treatment of a Pediatric Patient with Wolff-Hirschorn Syndrome under General Anesthesia -A Case Report-  

Shin, Seung-Woo (Department of Pediatric Dentistry, School of Dentistry, Dankook University)
Kim, Jong-Soo (Department of Pediatric Dentistry, School of Dentistry, Dankook University)
Kim, Seung-Oh (Department of Dental Anesthesia, School of Dentistry, Dankook University)
Publication Information
Journal of The Korean Dental Society of Anesthesiology / v.11, no.1, 2011 , pp. 51-54 More about this Journal
Abstract
Wolff-Hirschorn syndrome is a condition that is caused by a deletion of genetic material near the end of the short (p) arm of chromosome 4. The major features of this disorder include a characteristic facial appearance, delayed growth and development, intellectual disability, and seizures. A 9-year-old girl was brought to the clinic with a chief complaint of dental examination. The child was diagnosed as WHS at Samsung medical center. The child was under Sodium valproate, Atrovastatin medication for epilepsy, hyperlipidemia and had a history of heart surgery. So prophylactic antibiotics were recommended. The child was mentally retarded and had seizure so it was difficult to manage her behavior effectively. Thus dental treatment was carried out under general anesthesia. For prompt sedation induction we used 8% sevoflurane shortly. This report presents the case of a 9-year-old girl with WHS, who has received treatment for extensive caries under general anesthesia.
Keywords
Wolff-Hirschorn syndrome; General anesthesia; Prophylactic antibiotics; 8% sevoflurane induction;
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