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Ambulatory Anesthesia Management of the Patient with Adrenoleukodystrophy for Dental Treatment -A Case Report-  

Seo, Kwang-Suk (Department of Dental Anesthesiology, Seoul National University, School of Dentistry)
Bak, So-Yeon (Department of Pediatric Dentistry, Seoul National University, School of Dentistry)
Shin, Teo-Jeon (Department of Dental Anesthesiology, Seoul National University, School of Dentistry)
Kim, Hyun-Jeong (Department of Dental Anesthesiology, Seoul National University, School of Dentistry)
Publication Information
Journal of The Korean Dental Society of Anesthesiology / v.10, no.1, 2010 , pp. 45-49 More about this Journal
Abstract
Adrenoleukodystrophy (ALD) is a rare X-linked genetic disorder associated with various central nervous system problems and adrenal insufficiency. It is common in childhood and symptoms include loss of previously acquired neurological abilities, seizures, ataxia, Addison's disease as well as degeneration of visual and auditory function. These children frequently require anesthesia during imagining procedure such as MRI or during some surgical procedures like gastrostomy. There is special need for careful management because of numerous anesthetic challenges like difficulty in cooperation, seizure disorders, life-threatening airway obstruction, copious oral secretion and possibility of aspiration. In addition, adrenal involvement and hypofunction must be considered for safe anesthesia management. We report a successful anesthetic management in a patient with ALD for dental procedures.
Keywords
Adrenoleukodystrophy (ALD) Dental treatment; General Anesthesia; Cooperation difficulty;
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