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http://dx.doi.org/10.4047/jap.2015.7.5.406

Prosthetic management of a growing patient with Russell-Silver syndrome: a clinical report  

Kim, Kanghyun (Department of Prosthodontics, School of Dentistry, Kyung Hee University)
Noh, Kwantae (Department of Prosthodontics, School of Dentistry, Kyung Hee University)
Paek, Janghyun (Department of Prosthodontics, School of Dentistry, Kyung Hee University)
Kwon, Kung-Rock (Department of Prosthodontics, School of Dentistry, Kyung Hee University)
Pae, Ahran (Department of Prosthodontics, School of Dentistry, Kyung Hee University)
Publication Information
The Journal of Advanced Prosthodontics / v.7, no.5, 2015 , pp. 406-410 More about this Journal
Abstract
Russell-Silver syndrome (RSS) is a congenital disease characterized by short stature due to growth hormone deficiency, physical asymmetry, inverted triangular face, micrognathia, prominent forehead, and hypodontia. This case report presents a prosthetic management of a 6-year-old patient with Russell-Silver syndrome treated with overdentures on the maxilla and the mandible using the remaining primary teeth. Subsequent and comprehensive dental management considering the growth and development of a young patient will be necessary.
Keywords
Russell-Silver syndrome; Hypodontia; Overdenture; Early prosthetic rehabilitation;
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