대한영상의학회지 (Journal of the Korean Society of Radiology)

  • 제85권2호
  • /
  • Pages.451-455
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  • 2024
  • /
  • 1738-2637(pISSN)
  • /
  • 2288-2928(eISSN)
대한영상의학회 (The Korean Society of Radiology)
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고함-스타우트병과 연관된 유미흉 치료에서 림프관 색전술의 역할: 증례 보고

Role of Lymphatic Embolization in Chylothorax Associated with Gorham-Stout Disease: A Case Report

  • 유민혁 (성균관대학교 의과대학 삼성서울병원 영상의학과) ;
  • 현동호 (성균관대학교 의과대학 삼성서울병원 영상의학과) ;
  • 신선혜 (성균관대학교 의과대학 삼성서울병원 호흡기내과) ;
  • 하상윤 (성균관대학교 의과대학 삼성서울병원 병리과)
  • Min-Hyuk Yu (Department of Radiology, Samsung Medical Center, Sungkyunkwan University School of Medicine) ;
  • Dongho Hyun (Department of Radiology, Samsung Medical Center, Sungkyunkwan University School of Medicine) ;
  • Sun-Hye Shin (Division of Pulmonary and Critical Care Medicine, Samsung Medical Center, Sungkyunkwan University School of Medicine) ;
  • Sang-Yun Ha (Department of Pathology, Samsung Medical Center, Sungkyunkwan University School of Medicine)
  • 투고 : 2023.04.24
  • 심사 : 2023.08.18
  • 발행 : 2024.03.01
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초록

특이 외상력 없이 우측 1, 2번 갈비뼈 골용해와 자발성 유미흉을 주소로 내원한 45세 남환이 임상 양상과 골생검을 통해 고함-스타우트병으로 확진된 증례를 보고하고자 한다. 자발성 유미흉의 치료를 위해 림프관 색전술을 시행하였고 성공적인 시술 직후 유미흉은 호전되었다. 하지만 15개월간의 관찰 동안 시롤리무스(sirolimus) 투여에도 불구하고 유미흉이 재발되었고 흉부 불편감과 골용해는 진행되었다.

A 45-year-old male patient with spontaneous chylothorax and osteolysis in the right 1st and 2nd ribs was diagnosed with Gorham-Stout disease based on clinical manifestations and bone biopsy. The chylothorax temporarily decreased after a successful selective lymphatic embolization. The patient presented with recurrent chylothorax, mild chest discomfort, and progressive osteolysis (despite administering sirolimus) during the follow-up period of 15 months.

키워드

참고문헌

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