Journal of the Korean Society of Radiology (대한영상의학회지)

The Korean Society of Radiology (대한영상의학회)
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Treating Sudden Onset Hepatic Encephalopathy with Coil Embolization in a Patient with a Congenital Intrahepatic Portosystemic Venous Shunt: A Case Report

갑자기 간성뇌증이 발생한 선천성 간내 문맥정맥단락 환자의 코일 색전술 치료: 증례 보고

  • Yeonsoo Choi (Department of Radiology, Pusan National University Yangsan Hospital) ;
  • Jin Hyeok Kim (Department of Radiology, Pusan National University Yangsan Hospital) ;
  • Ung Bae Jeon (Department of Radiology, Pusan National University Yangsan Hospital) ;
  • Joo Yeon Jang (Department of Radiology, Pusan National University Yangsan Hospital) ;
  • Tae Un Kim (Department of Radiology, Pusan National University Yangsan Hospital) ;
  • Hwaseong Ryu (Department of Radiology, Pusan National University Yangsan Hospital)
  • 최연수 (양산부산대학교병원 영상의학과) ;
  • 김진혁 (양산부산대학교병원 영상의학과) ;
  • 전웅배 (양산부산대학교병원 영상의학과) ;
  • 장주연 (양산부산대학교병원 영상의학과) ;
  • 김태언 (양산부산대학교병원 영상의학과) ;
  • 류화성 (양산부산대학교병원 영상의학과)
  • Received : 2022.02.03
  • Accepted : 2022.05.01
  • Published : 2022.11.01
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Abstract

Intrahepatic portosystemic venous shunt (IPSVS) is a rare vascular abnormality that involves abnormal communication between the intrahepatic portal vein and systemic veins, such as the hepatic vein or inferior vena cava. Patients with IPSVS are typically asymptomatic, and IPSVS is incidentally discovered via imaging while evaluating other diseases. However, endovascular closure of the shunt should be considered in symptomatic patients with a high-flow shunt. This report presents a patient with congenital IPSVS with sudden onset hepatic encephalopathy treated using percutaneous transhepatic embolization.

간내 문맥정맥단락은 간문맥-대정맥 또는 간문맥-간정맥이 연결되어 있는 드문 혈관 질환이다. 간내 문맥정맥단락은 주로 무증상을 보이며, 다른 질환으로 영상 검사를 하였을 때 우연히 발견될 수 있다. 하지만 단락양이 많거나 증상이 있는 경우 단락 색전술을 고려하여야 한다. 저자들은 선천성 간내 문맥정맥단락 환자에서 갑자기 간성뇌증이 발생하여 이를 경간 코일 색전술로 치료한 증례를 보고하고자 한다.

Keywords

Acknowledgement

This study was supported by a 2022 research grant from Pusan National University Yangsan Hospital.

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