대한영상의학회지 (Journal of the Korean Society of Radiology)

  • 제83권6호
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  • Pages.1373-1379
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  • 2022
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  • 1738-2637(pISSN)
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  • 2288-2928(eISSN)
대한영상의학회 (The Korean Society of Radiology)
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우측기관주위의 종격동 종괴로 나타난 상피양 혈관내피종: 증례 보고

Epithelioid Hemangioendothelioma Presenting as a Right Paratracheal Mass: A Case Report

  • 홍파 (성균관대학교 의과대학 삼성창원병원 영상의학과) ;
  • 이재석 (성균관대학교 의과대학 삼성창원병원 병리과) ;
  • 이경수 (성균관대학교 의과대학 삼성창원병원 영상의학과)
  • Pa Hong (Department of Radiology, Samsung Changwon Hospital, Sunkyunkwan University School of Medicine (SKKU-SOM)) ;
  • Jae Seok Lee (Department of Pathology, Samsung Changwon Hospital, Sunkyunkwan University School of Medicine (SKKU-SOM)) ;
  • Kyung Soo Lee (Department of Radiology, Samsung Changwon Hospital, Sunkyunkwan University School of Medicine (SKKU-SOM))
  • 투고 : 2022.04.20
  • 심사 : 2022.06.01
  • 발행 : 2022.11.01
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초록

상피양 혈관내피종(epithelioid hemangioendothelioma)은 낮은 등급의 악성도를 가지는 혈관신생종양으로 신체의 어느 부위에나 발생할 수 있다. 상피양 혈관내피종은 매우 드문 발병률 및 유병률을 가지며, 종격동의 원발성 상피양 혈관내피종은 더욱 드물다. 우리는 우연히 발견된 우측 기관주위 종괴로 내원하여 상피양 혈관내피종을 진단받은 53세 여자 환자의 증례를 경험하였으며, 상대정맥을 침범한 원발성 종격동 상피양 혈관내피종의 병리학적, 영상의학적 소견을 보고한다.

Epithelioid hemangioendothelioma (EHE) is a low-grade malignant vascular neoplasm that can occur anywhere in the body. EHE has a low annual incidence (0.38/106) and prevalence (< 1/106), and primary mediastinal EHE is exceedingly rare. We report a case of EHE in a 53-year-old female which manifested as an incidentally discovered mass in the right paratracheal region. In this report, authors describe the pathological and radiological findings of primary mediastinal EHE invading the superior vena cava in the right paratracheal area.

키워드

참고문헌

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